ABSTRACT

Pulmonary agenesis is a rare congenital anomaly, consisting of complete absence of the lung parenchyma, bronchi, and pulmonary vessels. The cause is unknown. In 50% of cases, especially in cases of right lung agenesis, cardiovascular, musculoskeletal, gastrointestinal, and renal malformations are also present. The prognosis is better in cases of left lung agenesis and when there is no cardiac malformation. Herein, we report the clinical case of a 5-year-old boy with left lung agenesis, without any other congenital malformations.